Genetics and biomarkers

The molecular map concentrates in collagen and collagen-processing pathways

establishedfinding

Confirmed subtype genes cluster into collagen structure (COL5A1/A2, COL3A1, COL1A1/A2, COL12A1), collagen processing (ADAMTS2, PLOD1), proteoglycan and glycosaminoglycan pathways (B4GALT7, B3GALT6, CHST14, DSE), complement (C1R, C1S), and signaling (TNXB, SLC39A13, ZNF469, PRDM5, FKBP14). The 2017 classification groups subtypes by shared pathway for research purposes.

Subtype scopeall EDS types
Criteria erainternational-2017
Reviewed2026-09-16

Evidence

clinicalconsensus statement